Indian Journal of Physical Medicine and Rehabilitation

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VOLUME 24 , ISSUE 4 ( December, 2013 ) > List of Articles

CASE REPORT

Plexiform Neurofibromatosis with Abnormal Pachydermatocele: A Rare Case Report

AK Agarwal, Dileep Kumar, Anil Kumar Gupta, Ganesh Yadav

Citation Information : Agarwal A, Kumar D, Gupta AK, Yadav G. Plexiform Neurofibromatosis with Abnormal Pachydermatocele: A Rare Case Report. Indian J Phy Med Rehab 2013; 24 (4):110-113.

DOI: 10.5005/ijopmr-24-4-110

Published Online: 00-12-2013

Copyright Statement:  Copyright © 2013; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Plexiform neurofibromatosis, also known as pachydermatocele, is a rare type of neurofibromatosis, caused by excessive growth of the neural tissue in the subcutaneous fat. This condition is rare in Indian subcontinent but when it occurs, it causes cosmetic as well as functional disability. The optimal management of plexiform neurofibroma is not well defined and surgery is often delayed. We report a rare case of neurofibromatosis with pachydermatocele involving the nerves of the left thigh and leg with disfigurement and associated disability.


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